Leiomyosarcoma of the inferior vena cava
نویسندگان
چکیده
Leiomyosarcoma (LMS) is a mesenchymal tumor that originates from the smooth cells of vessel wall; it accounts for 6% of all sarcomas and 15% of sarcomas of the soft retroperitoneal tissue. It is the most frequent mesenchymal tumor of the large vessels, occurring in among 50% of cases in the inferior vena cava (IVC). Pulmonary artery and thoracic aorta are following frequent location1. More than 80% of cases are females, most of them between fifth and sixth decades, while males are rarely and lately affected (seventh decade). IVC leiomyosarcoma are classified anatomically according to their relationship to the liver and renal vessels: lower or segment 1 (below the renal vessels), middle or segment 2 (from renal vessels to retrohepatic IVC) and upper or segment 3 (suprahepatic IVC). Since Perl’s first description of a LMS of the IVC in 18712, little more than 300 cases have been reported in English literature. The first successful operation was reported by Melchior in 19283. Surgical “en bloc” resection of tumor and vein is the mainstay of treatment.
منابع مشابه
A case of giant leiomyosarcoma of the inferior vena cava with liver metastases: A surgical challenge
Introduction: Leiomyosarcoma of the inferior vena cava is a rare tumor that is hard to diagnose because there are no definitive symptoms. Case Report: A 72-year-old Japanese female presented with edema in both legs. Enhanced computed tomography scan of the abdomen revealed a heterogeneous tumor measuring 10×11×15 cm, which exerted pressure on the inferior vena cava. We preoperatively diagnosed ...
متن کاملLeiomyosarcoma of the inferior vena cava propagating into the right atrium.
were leiomyosarcomas and only 1 was an endothelioma. Hoffbrand and Lloyd-Thomas (1964) reported 14 cases of leiomyosarcoma of the inferior vena cava and added a case of their own. We are not aware of any case reports in which the diagnosis of leiomyosarcoma of the inferior vena cava has been made before an operation. The purpose of this paper is to report a case of leiomyosarcoma, diagnosed in ...
متن کاملLeiomyosarcoma of inferior vena cava complicated by Budd-Chiari syndrome and disseminated intravascular coagulation
Leiomyosarcoma of inferior vena cava is a rare malignant mesenchymal tumor of the venous system that typically occurs in adulthood. Correct and early recognition of leiomyosarcoma is very important, because a complete resection of the tumor (with occasionally chemioor radiotherapy) can lead to prolonged survival. We report a case of a 54-year-old man suffering from the leiomyosarcoma of inferio...
متن کاملImaging of leiomyosarcoma of the inferior vena cava: comparison of 2 cases and review of the literature
Leiomyosarcoma of the inferior vena cava is a rare tumour arising from the smooth muscle fibres of the media with a mean size at diagnosis generally around 12 cm (range 2-38 cm). This study compares a 4-cm leiomyosarcoma of the inferior vena cava discovered incidentally with a symptomatic late stage leiomyosarcoma.
متن کاملInferior vena cava leiomyosarcoma: preoperative diagnosis and surgical management
Inferior vena cava (IVC) leiomyosarcoma is a rare malignant neoplasm more commonly seen in women in the fifth to sixth decade of life. Complete resection of the tumor with negative margins is the only therapeutical option that has demonstrated a survival benefit. This report presents a case of a 67-year-old woman affected by a lower segment IVC leiomyosarcoma incidentally detected during a chro...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
عنوان ژورنال:
دوره شماره
صفحات -
تاریخ انتشار 2008